|
KMID : 0388220070140020160
|
|
Journal of the Korean Rheumatism Association
2007 Volume.14 No. 2 p.160 ~ p.165
|
|
|
Two Cases of Adult Onset Still’s Disease with Concomitant Hemophagocytic Syndrome
|
|
Kim Hyun-Sook
Choe Jung-Yoon
Park Keun-Woo
Kim Ji-Young
Park Sung-Hoon
Shin Jin-Hyang
Kim Sang-Gyung
Kim Soo-Kyung
|
|
|
Abstract
|
|
|
|
Adult onset Still’s disease is an rare inflammatory disease with the characteristic of fever, skin rash, arthralgia or arthritis, lymphadenopathy, leukocytosis and multiple systemic organ involve-ment. Its accurate pathogenesis has not been elucidated yet. Its clinical manifestation is also very diverse, from relatively mild symptoms to severe complications such as concomitant in-fection, liver failure, disseminated intravascular coagulation, myocarditis, adult respiratory distress syndrome, which may lead to death in some cases. Particularly, concomitant hemophagocytic syndrome is rare complication that could induce a fatal outcome. Thus it is important to diagnose early and start treatments. Until now, it has been reported in only one case of adult onset Still’s disease in Korea. Here, we report two female cases of adult onset Still’s disease with con-comitant hemophagocytic syndrome.
|
|
|
KEYWORD
|
|
|
Adult onset Still’s disease (AOSD), Hemophagocytic syndrome
|
|
|
FullTexts / Linksout information
|
|
|
|
|
|
Listed journal information
|
|
  
|
|